Introduction: Cystic Fibrosis (CF) is a hereditary genetic disease of autosomal recessive
origin. Caused by failure in production and function of the transmembrane regulatory protein
that is linked to the transport of salt and water from cell membranes. Understanding the
nutritional status in patients with cystic fibrosis is of fundamental importance, since an
inadequate nutritional interpretation of the patient; can cause its mortality. Objective: To
evaluate the nutritional and biochemical status of children with cystic fibrosis seen at a
reference outpatient clinic in Belém-PA. Materials and Methods: This was a cross-sectional,
descriptive and analytical study, including children with confirmed CF diagnosis, treated at
the outpatient clinic of the João de Barros Barreto University Hospital / Federal University of
Pará (HUJBB / UFPA). Patients aged between 1 and 11 years, of both sexes, diagnosed with
CF, between June and September 2018, were analyzed. They were performed for
anthropometric (weight, stature, Imc / age), clinical and dietary parameters. Results: 66.7% of
the patients were male and 33.3% female; 86.7% used supplements and enzymes; 66.7% had
eutrophic condition and all biochemical data collected were within the recommended values;
There was a correlation between children with higher body weight and those with higher
cholesterol values, besides fasting glucose that was associated with total cholesterol and LDL.
Conclusion: Given the data obtained, there is a need for further studies that characterize the
nutritional profile and even implement nutritional interventions in patients with cystic
fibrosis, because the literature on the subject is still scarce.
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